Biliary Atresia Associated with Polysplenia Syndrome, Situs Inversus Abdominus, and Reverse Rotation of Intestine
نویسندگان
چکیده
In 25% of cases of biliary atresia associated malformations are present; polysplenia constitute 10-50% of these associated anomalies. Biliary atresia found associated with polysplenia syndrome, heterotaxy, and reverse rotation of intestine, in isolation or in various combinations; however its association with polysplenia syndrome, situs inversus abdominus, and reverse rotation of gut in the same patient is not reported in English language literature [1,2].
منابع مشابه
Polysplenia Syndrome Associated with Situs Inversus Abdominus and Type I Jejunal Atresia
Polysplenia is a presence of two or more spleens in a patient and polysplenia syndrome refers to its association with various organ abnormalities in abdomen and chest. In about 20% cases of polysplenia syndrome situs inversus is present [1]. Polysplenia syndrome in association with situs inversus abdominus and intestinal atresia is rarely reported. We are presenting a case of polysplenia syndro...
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